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Goula A, Berquist BR, Wilson DM, Wheeler VC, Trottier Y, Merienne K. Stoichiometry of Base Excision Repair Proteins Correlates with Increased Somatic CAG Instability in Striatum over Cerebellum in Huntington's Disease Transgenic Mice. PLoS Genet. 2009 Dec 04;5(12):e1000749. doi: 10.1371/journal.pgen.1000749. |