Kakhlon O, Glickstein H, Feinstein N, Liu Y, Baba O, Terashima T, Akman HO, DiMauro S, Lossos A. Polyglucosan neurotoxicity caused by glycogen branching enzyme deficiency can be reversed by inhibition of glycogen synthase. Journal of Neurochemistry. 2013 May 09;127(1):101–13. doi: 10.1111/jnc.12277.