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Thompson GN, Walter JH, Bresson JL, Ford GC, Bonnefont JP, Chalmers RA, Saudubray JM, Leonard JV, Halliday D. Substrate disposal in metabolic disease: a comparison between rates of in vivo propionate oxidation and urinary metabolite excretion in children with methylmalonic acidemia. J Pediatr. 1989 Nov;115(5 Pt 1):735–9. doi: 10.1016/s0022-3476(89)80651-1. PMID: 2809905. |