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filingDate 2001-08-24-04:00^^<http://www.w3.org/2001/XMLSchema#date>
inventor http://rdf.ncbi.nlm.nih.gov/pubchem/patentinventor/MD5_a118ab1a83422161264b8193b4481619
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publicationDate 2002-02-28-04:00^^<http://www.w3.org/2001/XMLSchema#date>
publicationNumber WO-0216417-A2
titleOfInvention Transgenic animal model for neurodegerative disease and uses thereof
abstract The invention provides a transgenic non-human mammal comprising nucleated cells containing a transgene encoding an ataxin-2 polypeptide comprising a polyglutamine tract. In particular, the transgenic-non-human mammal can be a mouse. The invention also provides methods of using a transgenic non-human mammal expressing SCA2 encoding an ataxin-2 polypeptide to identify a therapeutic agent for use in treating a neurodegenerative disease by administering a compound to a transgenic non-human mammal expressing SCA2 encoding an ataxin-2 polypeptide and screening the transgenic non-human mammal for an improved neurological response associated with a neurodegenerative phenotype of the transgenic non-human mammal, thereby identifying a therapeutic agent for use in treating the neurodegenerative disease.
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http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ00553
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ2QLH0
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ00554
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID8627545
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ00555
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID6712
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID226394092
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA4TLL5
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCB4S2K9
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ58D55
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCO69315
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ7TQD2
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID13498
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA8GGN3
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID776
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ59750
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCB7N8Q1
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA3FEW8
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ5U820
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID12638
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID34420
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID4287
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ5IS70
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ8X685
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ00PJ2
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID6310
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID136288194
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCB5XQY2
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID1080
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID9548661
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID6311
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ3Z583
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID6314
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID21226166
http://rdf.ncbi.nlm.nih.gov/pubchem/anatomy/ANATOMYID11757
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID739740
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID368667
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID565841
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA8AKB8
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA1SWB8
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP48980
http://rdf.ncbi.nlm.nih.gov/pubchem/taxonomy/TAXID36229
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID33629
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID745
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP48981
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP48982
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID122217
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID419551860
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ5R780
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ9TRY9
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID226396326
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID31624
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ8VNN2
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID226396327
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ9TSP5
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID29192
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP84589
http://rdf.ncbi.nlm.nih.gov/pubchem/taxonomy/TAXID43872
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID81822
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA0KQH4
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID18451662
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID2541030
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID158181059
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP54258
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID226412347
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP54259
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID226412348
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP69310
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID23636559
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ09YH0
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP00722
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP69313
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID850620
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ09YJ4
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID828213
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID816103
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP69317
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCD3ZQL7
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID419581356
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ09YK5
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ8SWD4
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP69326
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA7ZI91
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID100686650
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID135985134
http://rdf.ncbi.nlm.nih.gov/pubchem/anatomy/ANATOMYID36229
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCO52629
http://rdf.ncbi.nlm.nih.gov/pubchem/gene/GID773
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP22498
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ9W689
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID226393946
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ6D736
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ48727
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCO52847
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP14288
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ9W6T7
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID2118
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ03WL0
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ108U0
http://rdf.ncbi.nlm.nih.gov/pubchem/anatomy/ANATOMYID43872
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCA5F5U6
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ7JII7
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCP00723
http://rdf.ncbi.nlm.nih.gov/pubchem/compound/CID165271
http://rdf.ncbi.nlm.nih.gov/pubchem/substance/SID433322195
http://rdf.ncbi.nlm.nih.gov/pubchem/protein/ACCQ7JII8

Total number of triples: 413.